Melanotic Neuroectodermal Tumour of Infancy (Progonoma) Treated by Radical Maxillary Surgery
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Date
2009-06
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Publisher
Ghana Medical Journal
Abstract
Two cases of melanotic neuroectodermal tumour of
infancy (MNTI), otherwise known as melanotic progonoma,
both arising from the maxilla are presented here.
The two infants both presented within three months of
each other and though clinically Burkitt’s lymphoma
was stated as a possible diagnosis, the correct diagnosis
was made on biopsy specimens. Radical surgery consisting
of wide resection of the tumour with margins of
healthy tissue via hemi-maxillectomy was performed in
each case as an initial method of treatment. At follow
up four months later, both infants appeared clinically
well. One infant was then lost to follow up thereafter
but the other was reviewed three years later, and apart
from slight facial asymmetry, there was no evidence of
tumour recurrence.
Description
Journal Article
Keywords
Melanotic neuroectodermal tumour of infancy, melanotic progonoma, radical maxillary surgery